Congenital insensitivity to pain with anhidrosis (CIPA), also called hereditary sensory and autonomic neuropathy type IV (HSAN-IV), which is characterized by its inability to feel pain and temperature, and decreased or absence sweating which often leads to repeated severe injuries (“Genetics Home Reference- CIPA”, 2016).
However, patients with CIPA can still feel pressure. CIPA is the fourth
type of hereditary sensory and autonomic neuropathy which is a rare recessive
gene disorder caused by gene mutation. A person with CIPA cannot feel pain or
differentiate even extreme temperatures. By interpreting its name, "anhidrosis"
means the body does not sweat, and "congenital" indicates that the
condition is present from birth. Therefore, this also explains why signs and
symptoms of CIPA appear early, usually at birth or during infancy.
Read more here: https://ghr.nlm.nih.gov/condition/congenital-insensitivity-to-pain-with-anhidrosis#definition
Reference:
U.S. National Library of Medicine. (2016). Congenital insensitivity to pain with anhidrosis. U.S. National Library of Medicine. Retrieved October 13, 2016 from https://ghr.nlm.nih.gov/condition/congenital-insensitivity-to-pain-with-anhidrosis#definition
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